00957nam a2200229 c 4500001001300000005001500013007000300028008004100031041001300072049001800085052001700103056001300120082001500133100004800148245027400196260003900470300004800509502008700557504003100644546003400675900001800709KDM20126497420130110131718ta121018s2012 ulkad m AL 000 eng 0 aengbkor0 lWM718658fWDP02a618.92b12-3 a516.92501a618.922211 a손영배,g孫永培,d1979-0KAC20160363710aImprovement of CNS defects via continuous intrathecal enzyme replacement therapy in mucopolysaccharidosis typeⅡmice =x제 2형 뮤코다당체 침착증 쥐에서 지속적 척수강내 효소보충 치료를 통한 중추신경계 병변의 호전 /dYoung Bae Sohn aSeoul :bSungkyunkwan Univ.,c2012 aiv, 28 leaves :bcol. ill., charts ;c30 cm1 aThesis(Ph.D.) --bGraduate School, Sungkyunkwan Univ.,cDept. of Pediatrics,d2012 aBibliography: leaves 16-20 aIn English; summary in Korean10aSon, Yeongbae